Search results for "2731 Ophthalmology"

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Usherin defects lead to early-onset retinal dysfunction in zebrafish

2018

Mutations in USH2A are the most frequent cause of Usher syndrome and autosomal recessive nonsyndromic retinitis pigmentosa. To unravel the pathogenic mechanisms underlying USH2A-associated retinal degeneration and to evaluate future therapeutic strategies that could potentially halt the progression of this devastating disorder, an animal model is needed. The available Ush2a knock-out mouse model does not mimic the human phenotype, because it presents with only a mild and late-onset retinal degeneration. Using CRISPR/Cas9-technology, we introduced protein-truncating germline lesions into the zebrafish ush2a gene (ush2a(rmc1): c.2337_2342delinsAC; p.Cys780GlnfsTer32 and ush2a(b1245): c.15520_…

0301 basic medicineRetinal degenerationGenotyping TechniquesUsher syndrome2804 Cellular and Molecular NeuroscienceApoptosis030105 genetics & heredityBiologyArticleRetinaGermlineSensory disorders Donders Center for Medical Neuroscience [Radboudumc 12]Gene Knockout Techniques03 medical and health sciencesCellular and Molecular NeuroscienceUSH2 complex2809 Sensory SystemsAll institutes and research themes of the Radboud University Medical CenterRetinitis pigmentosaElectroretinographymedicineotorhinolaryngologic diseasesJournal ArticleAnimalsMicroscopy ImmunoelectronZebrafishZebrafishExtracellular Matrix ProteinsRetinal DegenerationMembrane ProteinsZebrafish ProteinsRetinal Photoreceptor Cell Outer Segmentmedicine.diseasebiology.organism_classification2731 OphthalmologySensory Systems10124 Institute of Molecular Life SciencesCell biologyDisease Models AnimalOphthalmology030104 developmental biologyGene Expression RegulationEctodomainMutation570 Life sciences; biologyXenotropic and Polytropic Retrovirus ReceptorUsher SyndromesErg
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Developmental changes in the microgenesis of face perception revealed by effects of context and inversion

2011

AbstractPresent studies on the development of face perception mechanisms are ambiguous about the question of whether holistic face vision arises early, or in the second decade of life (Crookes & McKone, 2009). Measuring the time course of face matching we assess effects of context and inversion as correlates of holistic processing in the microgenesis of face perception within the first 650ms, and compare among 8- to 10-year-old children and adults. Results for adults indicate dominance of holistic viewing at brief timings, which is gradually replaced by feature selective strategies enabling them to selectively attend either internal or external features, as demanded by instruction. For chil…

MaleHolistic processingFace perceptionFace matchingFace inversion effect2809 Sensory SystemsChild DevelopmentDiscrimination PsychologicalFace perceptionHumansContextual informationChild10093 Institute of PsychologyInformation processingRecognition PsychologyInversion (meteorology)2731 OphthalmologySensory SystemsOphthalmologyFaceTime courseVisual PerceptionFemale150 PsychologyPsychologySocial psychologyInternal and external featuresCognitive psychologyVision Research
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